Pulmonary hypertension is a clinically complex disease with a wide range of causes. Consequently, the symptoms it presents in patients are numerous and complicated. Typically, patients with increasing pulmonary hypertension may experience varying degrees of shortness of breath after activity, chest tightness, dizziness, as well as chest pain, palpitations, and fainting. Generally, it does not cause headaches. However, many cases of pulmonary hypertension might also involve conditions such as hypertension, or other diseases that could lead to headaches. When pulmonary hypertension is worsening, it might coincide with an increase in blood pressure, which could also trigger headaches at that time. Therefore, it is important to differentiate in clinical practice; primary pulmonary hypertension generally does not cause headaches but can cause dizziness.